Aortic and mitral valve surgery through a superior ministernotomy in pectus excavatum associated with Marfan's syndrome.
نویسندگان
چکیده
The combination of chest wall abnormalities such as pectus excavatum and cardiac disease requiring operative correction represents a clinical challenge to the surgeon. We report two cases of patients with Marfan's syndrome and severe pectus excavatum in whom cardiac operations were successfully performed using a superior 'T inverted' ministernotomy. This approach allowed safe isolation of the target cardiac structures, provided excellent operative exposure and enhanced chest wall stability by preserving the integrity of the lower sternum.
منابع مشابه
Combined mitral valve replacement associated with the Bentall procedure, diaphragmatic hernia repair and reconstruction of the pectus excavatum in a 26-year-old patient with Marfan syndrome
A 26-year-old man with Marfan syndrome was admitted as an emergency patient with ascending aorta aneurysm, severe mitral and aortic regurgitation, diaphragmatic hernia and pectus excavatum. After completion of diagnostics a combined surgical procedure was performed.
متن کاملPectus excavatum and MASS phenotype: an unknown association.
INTRODUCTION Severe pectus excavatum (PE) is a deep chest wall deformity that generates both a cosmetic damage and a cardiac/respiratory function impairment. Excluding the scarce reports on Marfan's syndrome (MFS) and Ehlers-Danlos's syndrome (EDS), few studies have examined the relation between severe PE and connective tissue disorders. The aim of this study is to verify the clinical significa...
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A 27-year-old man with Marfan syndrome was referred to our department for dilatation of the aortic root with mild aortic regurgitation. His past medical history was unremarkable. Physical examination was normal except for a pectus excavatum. Transthoracic ultrasounds scan showed normal left ventricular function, mild aortic and mitral regurgitation, and dilatation of the aortic root with maximu...
متن کاملAortic valve-sparing operation after correction of heart displacement due to pectus excavatum using Nuss procedure in a Marfan syndrome patient.
Cardiovascular surgery in the setting of chest wall deformities is a clinical challenge. Pectus excavatum, for example, can cause heart displacement to the left thoracic cavity, following the poor operative field. This report highlights a case in which a successful aortic valve-sparing operation via conventional median sternotomy after correction of the heart displacement due to pectus excavatu...
متن کاملSimultaneous mitral valve and pectus excavatum repair with a Nuss bar.
We present the successful management of an interesting case of a single-stage combined mitral valve repair plus repair of the pectus excavatum with a Nuss bar.
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عنوان ژورنال:
- Interactive cardiovascular and thoracic surgery
دوره 2 2 شماره
صفحات -
تاریخ انتشار 2003